A 20 year-old girl was admitted to our clinic in June, 1999 with a five-year history of cough and sputum production. Chest x- ray revealed nonhomogenous infiltrates in left lower paracardiac region. Bacteriological and biochemical tests and bronchoscopic examination were normal. High resolution computed tomography was performed which evidently indicated pulmonary sequestration findings and the diagnosis of pulmonary sequestration was confirmed by aortography. After thoracotomy and left lower lobectomy, the patient’s follow up was without complaints