A 73-year-old male patient presented with two mass lesions, a larger one in the right and another in the left lung. Fiberoptic bronchoscopic examination revealed a tabulated endobronchial lesion in the left upper lobe bronchus and normal findings in the right bronchial system. The histologic diagnosis of the endobronchial lesion was myxoma whereas transthoracic tru-cut biopsy performed from the mass lesion in the right lung revealed adenocarcinoma. Pulmonary myxomas are exceedingly rare tumors and there are very few reported cases of endobronchial myxoma. Thus we report the concomittant occurrence of lung cancer and a benign endobronchial myxoma.